{"id":28983,"date":"2025-04-16T10:32:21","date_gmt":"2025-04-16T01:32:21","guid":{"rendered":"https:\/\/www.marketresearch.jp\/reports\/?p=28983"},"modified":"2026-09-06T19:14:46","modified_gmt":"2026-09-06T10:14:46","slug":"plasma-protease-c1-inhibitor-market-gmi","status":"publish","type":"post","link":"https:\/\/www.marketresearch.jp\/reports\/plasma-protease-c1-inhibitor-market-gmi\/","title":{"rendered":"\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306e\u4e16\u754c\u5e02\u5834\uff082025-2034\uff09\uff1a\u85ac\u52b9\u30af\u30e9\u30b9\u5225\uff08\u8840\u6f3f\u7531\u6765C1\u963b\u5bb3\u5264\u3001\u9078\u629e\u7684\u30d6\u30e9\u30b8\u30ad\u30cb\u30f3B2\u53d7\u5bb9\u4f53\u62ee\u6297\u85ac\u3001\u30ab\u30ea\u30af\u30ec\u30a4\u30f3\u963b\u5bb3\u5264\uff09\u3001\u5264\u5f62\u5225\u3001\u6d41\u901a\u30c1\u30e3\u30cd\u30eb\u5225"},"content":{"rendered":"

\"\"<\/p>\n

\u7b2c1\u7ae0 \u65b9\u6cd5\u8ad6\u3068\u7bc4\u56f2
\n1.1 \u5e02\u5834\u7bc4\u56f2\u3068\u5b9a\u7fa9
\n1.2 \u8abf\u67fb\u30c7\u30b6\u30a4\u30f3
\n1.2.1 \u8abf\u67fb\u30a2\u30d7\u30ed\u30fc\u30c1
\n1.2.2 \u30c7\u30fc\u30bf\u53ce\u96c6\u65b9\u6cd5
\n1.3 \u30d9\u30fc\u30b9\u3068\u306a\u308b\u63a8\u5b9a\u3068\u8a08\u7b97
\n1.3.1 \u57fa\u6e96\u5e74\u306e\u7b97\u51fa
\n1.3.2 \u5e02\u5834\u63a8\u8a08\u306e\u4e3b\u8981\u30c8\u30ec\u30f3\u30c9
\n1.4 \u4e88\u6e2c\u30e2\u30c7\u30eb
\n1.5 \u4e00\u6b21\u8abf\u67fb\u3068\u691c\u8a3c
\n1.5.1 \u4e00\u6b21\u60c5\u5831\u6e90
\n1.5.2 \u30c7\u30fc\u30bf\u30de\u30a4\u30cb\u30f3\u30b0\u30bd\u30fc\u30b9
\n\u7b2c2\u7ae0 \u30a8\u30b0\u30bc\u30af\u30c6\u30a3\u30d6\u30b5\u30de\u30ea\u30fc
\n2.1 \u696d\u754c360\u00b0\u306e\u6982\u8981
\n\u7b2c3\u7ae0 \u696d\u754c\u30a4\u30f3\u30b5\u30a4\u30c8
\n3.1 \u696d\u754c\u30a8\u30b3\u30b7\u30b9\u30c6\u30e0\u5206\u6790
\n3.2 \u696d\u754c\u306e\u5f71\u97ff\u529b
\n3.2.1 \u6210\u9577\u30c9\u30e9\u30a4\u30d0\u30fc
\n3.2.1.1 \u907a\u4f1d\u6027\u8840\u7ba1\u6027\u6d6e\u816b\uff08HAE\uff09\u304a\u3088\u3073\u88dc\u4f53\u7cfb\u969c\u5bb3\u306e\u6709\u75c5\u7387\u306e\u4e0a\u6607
\n3.2.1.2 \u30d0\u30a4\u30aa\u30c6\u30af\u30ce\u30ed\u30b8\u30fc\u3068\u533b\u85ac\u54c1\u958b\u767a\u306e\u9032\u6b69
\n3.2.1.3 \u653f\u5e9c\u306e\u597d\u610f\u7684\u306a\u898f\u5236\u304a\u3088\u3073\u511f\u9084\u653f\u7b56
\n3.2.1.4 \u5e0c\u5c11\u75be\u60a3\u306e\u7814\u7a76\u958b\u767a\u3078\u306e\u6295\u8cc7\u306e\u5897\u52a0
\n3.2.2 \u696d\u754c\u306e\u843d\u3068\u3057\u7a74\u3068\u8ab2\u984c
\n3.2.2.1 C1\u963b\u5bb3\u5264\u6cbb\u7642\u306e\u9ad8\u30b3\u30b9\u30c8
\n3.2.2.2 \u9650\u3089\u308c\u305f\u5165\u624b\u53ef\u80fd\u6027\u3068\u30b5\u30d7\u30e9\u30a4\u30c1\u30a7\u30fc\u30f3\u306e\u5236\u7d04
\n3.3 \u6210\u9577\u53ef\u80fd\u6027\u306e\u5206\u6790
\n3.4 \u85ac\u4e8b\u898f\u5236
\n3.5 \u30ae\u30e3\u30c3\u30d7\u5206\u6790
\n3.6 \u7279\u8a31\u5206\u6790
\n3.7 \u30d1\u30a4\u30d7\u30e9\u30a4\u30f3\u5206\u6790
\n3.8 \u30dd\u30fc\u30bf\u30fc\u5206\u6790
\n3.9 PESTEL\u5206\u6790
\n\u7b2c4\u7ae0 \u7af6\u4e89\u74b0\u5883\uff082024\u5e74
\n4.1 \u306f\u3058\u3081\u306b
\n4.2 \u4f01\u696d\u30b7\u30a7\u30a2\u5206\u6790
\n4.3 \u4f01\u696d\u30de\u30c8\u30ea\u30c3\u30af\u30b9\u5206\u6790
\n4.4 \u4e3b\u8981\u5e02\u5834\u30d7\u30ec\u30fc\u30e4\u30fc\u306e\u7af6\u5408\u5206\u6790
\n4.5 \u7af6\u5408\u306e\u30dd\u30b8\u30b7\u30e7\u30cb\u30f3\u30b0\u30de\u30c8\u30ea\u30c3\u30af\u30b9
\n4.6 \u6226\u7565\u30c0\u30c3\u30b7\u30e5\u30dc\u30fc\u30c9
\n\u7b2c5\u7ae0 2021\u301c2034\u5e74\u85ac\u52b9\u5206\u985e\u5225\u5e02\u5834\u63a8\u5b9a\u30fb\u4e88\u6e2c\uff08\u5358\u4f4d\uff1a\u767e\u4e07\u30c9\u30eb\uff09
\n5.1 \u4e3b\u8981\u30c8\u30ec\u30f3\u30c9
\n5.2 \u8840\u6f3f\u7531\u6765C1\u963b\u5bb3\u85ac
\n5.3 \u9078\u629e\u7684\u30d6\u30e9\u30b8\u30ad\u30cb\u30f3B2\u53d7\u5bb9\u4f53\u62ee\u6297\u85ac
\n5.4 \u30ab\u30ea\u30af\u30ec\u30a4\u30f3\u963b\u5bb3\u85ac
\n\u7b2c6\u7ae0 \u6295\u4e0e\u5f62\u614b\u5225\u5e02\u5834\u4e88\u6e2c\uff1a2021\u301c2034\u5e74\uff08$ Mn\uff09
\n6.1 \u4e3b\u8981\u30c8\u30ec\u30f3\u30c9
\n6.2 \u51cd\u7d50\u4e7e\u71e5\u5264
\n6.3 \u6ce8\u5c04\u5264
\n\u7b2c7\u7ae0 2021\u301c2034\u5e74\u6d41\u901a\u30c1\u30e3\u30cd\u30eb\u5225\u5e02\u5834\u4e88\u6e2c\u30fb\u4e88\u6e2c \uff08$ Mn\uff09
\n7.1 \u4e3b\u8981\u52d5\u5411
\n7.2 \u75c5\u9662\u85ac\u5c40
\n7.3 \u5c0f\u58f2\u85ac\u5c40
\n7.4 E\u30b3\u30de\u30fc\u30b9
\n\u7b2c8\u7ae0 2021\u301c2034\u5e74\u5730\u57df\u5225\u5e02\u5834\u4e88\u6e2c\u30fb\u4e88\u6e2c \uff08$ Mn\uff09
\n8.1 \u4e3b\u8981\u52d5\u5411
\n8.2 \u5317\u7c73
\n8.2.1 \u30a2\u30e1\u30ea\u30ab
\n8.2.2 \u30ab\u30ca\u30c0
\n8.3 \u30e8\u30fc\u30ed\u30c3\u30d1
\n8.3.1 \u30c9\u30a4\u30c4
\n8.3.2 \u30a4\u30ae\u30ea\u30b9
\n8.3.3 \u30d5\u30e9\u30f3\u30b9
\n8.3.4 \u30b9\u30da\u30a4\u30f3
\n8.3.5 \u30a4\u30bf\u30ea\u30a2
\n8.3.6 \u30aa\u30e9\u30f3\u30c0
\n8.4 \u30a2\u30b8\u30a2\u592a\u5e73\u6d0b
\n8.4.1 \u4e2d\u56fd
\n8.4.2 \u65e5\u672c
\n8.4.3 \u30a4\u30f3\u30c9
\n8.4.4 \u30aa\u30fc\u30b9\u30c8\u30e9\u30ea\u30a2
\n8.4.5 \u97d3\u56fd
\n8.5 \u30e9\u30c6\u30f3\u30a2\u30e1\u30ea\u30ab
\n8.5.1 \u30d6\u30e9\u30b8\u30eb
\n8.5.2 \u30e1\u30ad\u30b7\u30b3
\n8.5.3 \u30a2\u30eb\u30bc\u30f3\u30c1\u30f3
\n8.6 \u4e2d\u6771\u30fb\u30a2\u30d5\u30ea\u30ab
\n8.6.1 \u5357\u30a2\u30d5\u30ea\u30ab
\n8.6.2 \u30b5\u30a6\u30b8\u30a2\u30e9\u30d3\u30a2
\n8.6.3 \u30a2\u30e9\u30d6\u9996\u9577\u56fd\u9023\u90a6
\n\u7b2c9\u7ae0 \u4f01\u696d\u30d7\u30ed\u30d5\u30a3\u30fc\u30eb
\n9.1 Astria
\n9.2 BioCryst Pharmaceuticals
\n9.3 CSL Behring
\n9.4 Fresenius Kabi
\n9.5 Ionis Pharmaceuticals
\n9.6 KalVista
\n9.7 Pharming
\n9.8 Pharvaris
\n9.9 Takeda Pharmaceutical Company<\/p>\n

\"\"<\/p>\n","protected":false},"excerpt":{"rendered":"

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\u3055\u3089\u306b\u3001HAE\u3001\u305d\u306e\u75c7\u72b6\u3001\u8a3a\u65ad\u3001\u6cbb\u7642\u306e\u9078\u629e\u80a2\u306b\u5bfe\u3059\u308b\u8a8d\u8b58\u306e\u9ad8\u307e\u308a\u304c\u3001\u65e9\u671f\u8a3a\u65ad\u3068\u6cbb\u7642\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u85ac\u6cbb\u7642\u306f\u3001HAE\u60a3\u8005\u3067\u6a5f\u80fd\u4e0d\u5168\u306b\u9665\u3063\u3066\u3044\u308b\u88dc\u4f53\u7cfb\u306e\u5fc5\u8981\u306a\u5236\u5fa1\u3092\u56de\u5fa9\u3055\u305b\u308b\u3053\u3068\u3067\u3001HAE\u767a\u4f5c\u306e\u58ca\u6ec5\u7684\u306a\u5f71\u97ff\u306e\u4e88\u9632\u3068\u7ba1\u7406\u306b\u5f79\u7acb\u3061\u307e\u3059\u3002\u3055\u3089\u306b\u3001\u65b0\u898f\u306e\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u85ac\u306b\u5bfe\u3059\u308b\u898f\u5236\u5f53\u5c40\u306e\u627f\u8a8d\u3068\u5e0c\u5c11\u75be\u75c5\u7528\u533b\u85ac\u54c1\u306e\u6307\u5b9a\u304c\u3001\u5e02\u5834\u306e\u6210\u9577\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002\u4f8b\u3048\u3070\u30012023\u5e745\u6708\u3001\u30c1\u30ea\u306e\u516c\u8846\u885b\u751f\u7814\u7a76\u6240\uff08ISP\uff09\u306f\u300112\u6b73\u4ee5\u4e0a\u306eHAE\u767a\u4f5c\u3092\u9069\u5fdc\u75c7\u3068\u3059\u308bBioCryst Pharmaceuticals\u306eORLADEYO\uff08berotralstat\uff09\u6cbb\u7642\u85ac\u306e\u8ca9\u58f2\u627f\u8a8d\u3092\u4ed8\u4e0e\u3057\u307e\u3057\u305f\u3002<\/p>\n

\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306e\u5e02\u5834\u52d5\u5411
\n\u540c\u5e02\u5834\u3067\u306f\u3001\u60a3\u8005\u81ea\u8eab\u304c\u81ea\u5b85\u3067C1\u963b\u5bb3\u85ac\u3092\u6295\u4e0e\u3067\u304d\u308b\u3088\u3046\u306b\u3059\u308b\u3053\u3068\u3067\u3001\u30a2\u30c9\u30d2\u30a2\u30e9\u30f3\u30b9\u3068\u5229\u4fbf\u6027\u3092\u5411\u4e0a\u3055\u305b\u308b\u76ae\u4e0b\u6ce8\u88fd\u5264\u3078\u306e\u9700\u8981\u304c\u9ad8\u307e\u3063\u3066\u3044\u307e\u3059\u3002\u3053\u308c\u306f\u3001\u5165\u9662\u304c\u5fc5\u8981\u306a\u5f93\u6765\u306e\u9759\u8108\u5185\u8f38\u6db2\u306b\u4ee3\u308f\u308b\u3082\u306e\u3068\u3057\u3066\u597d\u307e\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u30d2\u30c8\u8840\u6f3f\u3078\u306e\u4f9d\u5b58\u3092\u4f4e\u6e1b\u3059\u308b\u907a\u4f1d\u5b50\u7d44\u63db\u3048\u7642\u6cd5\u306f\u3001\u73fe\u5728\u3001\u5f93\u6765\u306e\u8840\u6f3f\u7531\u6765\u306eC1\u963b\u5bb3\u85ac\u306b\u53d6\u3063\u3066\u4ee3\u308f\u308a\u3001\u3042\u308b\u3044\u306f\u305d\u308c\u3092\u88dc\u5b8c\u3057\u3066\u3044\u307e\u3059\u3002\u3055\u3089\u306b\u3001\u30d7\u30ed\u30c6\u30a2\u30fc\u30bc\u963b\u5bb3\u5264\u306e\u5408\u6210\u306b\u95a2\u9023\u3059\u308b\u907a\u4f1d\u5b50\u3092\u6539\u5909\u3057\u3001\u9577\u671f\u7684\u3042\u308b\u3044\u306f\u6839\u6cbb\u7684\u306a\u6cbb\u7642\u3092\u53ef\u80fd\u306b\u3059\u308b\u907a\u4f1d\u5b50\u6cbb\u7642\u3082\u691c\u8a0e\u3055\u308c\u3066\u3044\u307e\u3059\u3002\u4f8b\u3048\u3070\u3001\u30a4\u30aa\u30cb\u30b9\u30fb\u30d5\u30a1\u30fc\u30de\u30b7\u30e5\u30fc\u30c6\u30a3\u30ab\u30eb\u30ba\u3068\u6b66\u7530\u85ac\u54c1\u5de5\u696d\u306f\u3001\u30d7\u30ed\u30c6\u30a2\u30fc\u30bc\u6d3b\u6027\u3092\u8abf\u7bc0\u3059\u308b\u30a2\u30f3\u30c1\u30bb\u30f3\u30b9\u30fb\u30aa\u30ea\u30b4\u30cc\u30af\u30ec\u30aa\u30c1\u30c9\u7642\u6cd5\u306e\u53ef\u80fd\u6027\u3092\u7814\u7a76\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u3092\u795e\u7d4c\u75be\u60a3\u3001\u81ea\u5df1\u514d\u75ab\u75be\u60a3\u3001\u865a\u8840\u518d\u704c\u6d41\u969c\u5bb3\u3001\u6557\u8840\u75c7\u306a\u3069\u306e\u65b0\u305f\u306a\u7528\u9014\u306b\u62e1\u5927\u3059\u308b\u3053\u3068\u3092\u76ee\u7684\u3068\u3057\u305f\u7814\u7a76\u958b\u767a\uff08R&D\uff09\u306e\u53d6\u308a\u7d44\u307f\u3082\u6d3b\u767a\u5316\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u6210\u9577\u3059\u308b\u533b\u7642\u30a4\u30f3\u30d5\u30e9\u3001\u6d77\u5916\u304b\u3089\u306e\u6295\u8cc7\u3001HAE\u306b\u95a2\u3059\u308b\u610f\u8b58\u306e\u9ad8\u307e\u308a\u3001\u4fdd\u967a\u9069\u7528\u7bc4\u56f2\u306e\u62e1\u5927\u304c\u3001\u30a2\u30b8\u30a2\u592a\u5e73\u6d0b\u5730\u57df\u3068\u4e2d\u5357\u7c73\u5730\u57df\u306b\u304a\u3051\u308b\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306e\u63a1\u7528\u62e1\u5927\u3068\u7814\u7a76\u958b\u767a\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002\u5e02\u5834\u30d7\u30ec\u30a4\u30e4\u30fc\u306f\u3001\u672a\u958b\u62d3\u306e\u5e02\u5834\u6a5f\u4f1a\u3092\u7372\u5f97\u3059\u308b\u305f\u3081\u3001\u65b0\u898f\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u3084\u898f\u5236\u5f53\u5c40\u306e\u627f\u8a8d\u53d6\u5f97\u306b\u53d6\u308a\u7d44\u3093\u3067\u3044\u307e\u3059\u3002<\/p>\n

\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u85ac\u5e02\u5834\u306e\u5206\u6790
\n\u85ac\u5264\u30af\u30e9\u30b9\u306b\u57fa\u3065\u304d\u3001\u5e02\u5834\u306f\u8840\u6f3f\u7531\u6765C1\u963b\u5bb3\u5264\u3001\u9078\u629e\u7684\u30d6\u30e9\u30b8\u30ad\u30cb\u30f3B2\u53d7\u5bb9\u4f53\u62ee\u6297\u5264\u3001\u30ab\u30ea\u30af\u30ec\u30a4\u30f3\u963b\u5bb3\u5264\u306b\u533a\u5206\u3055\u308c\u307e\u3059\u3002\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306e\u4e16\u754c\u5e02\u5834\u898f\u6a21\u306f2023\u5e74\u306b16\u5104\u7c73\u30c9\u30eb\u3002\u8840\u6f3f\u7531\u6765C1\u963b\u5bb3\u5264\u30bb\u30b0\u30e1\u30f3\u30c8\u306f\u30012024\u5e74\u306b59.7%\u3068\u3044\u3046\u6700\u5927\u306e\u58f2\u4e0a\u30b7\u30a7\u30a2\u3067\u5e02\u5834\u3092\u652f\u914d\u3057\u307e\u3057\u305f\u3002<\/p>\n

HAE\u306e\u7f79\u60a3\u7387\u306e\u5897\u52a0\u306f\u3001\u4e88\u6e2c\u671f\u9593\u306b\u304a\u3051\u308b\u8840\u6f3f\u7531\u6765C1\u963b\u5bb3\u5264\u30bb\u30b0\u30e1\u30f3\u30c8\u306e\u91cd\u8981\u306a\u4fc3\u9032\u8981\u56e0\u3067\u3059\u3002\u4f8b\u3048\u3070\u3001Discover HAE\u306b\u3088\u308b\u3068\u30012022\u5e74\u306b\u306f\u4e16\u754c\u3067\u7d041,64,201\u4eba\u304cHAE\u306b\u7f79\u60a3\u3057\u3066\u3044\u307e\u3059\u3002\u3053\u306e\u9ad8\u3044\u7f79\u60a3\u7387\u306f\u3001\u52b9\u679c\u7684\u306a\u907a\u4f1d\u6027\u8840\u7ba1\u6027\u6d6e\u816b\u6cbb\u7642\u85ac\u306e\u5fc5\u8981\u6027\u3092\u5f37\u8abf\u3057\u3001\u5e02\u5834\u306e\u6210\u9577\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u8840\u6f3f\u7531\u6765\u306eC1\u963b\u5bb3\u5264\u306e\u7528\u9014\u304c\u62e1\u5927\u3057\u3066\u3044\u308b\u3053\u3068\u3082\u3001\u3053\u306e\u30bb\u30b0\u30e1\u30f3\u30c8\u306e\u58f2\u4e0a\u6210\u9577\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002\u4f8b\u3048\u3070\u30012022\u5e744\u6708\u3001\u30a2\u30e1\u30ea\u30abFDA\u306f\u3001\u30b7\u30f3\u30e9\u30a4\u30ba\u304cHAE\u60a3\u8005\u306e\u8840\u7ba1\u6027\u6d6e\u816b\u767a\u4f5c\u306b\u5bfe\u3059\u308b\u65e5\u5e38\u7684\u306a\u4e88\u9632\u85ac\u3068\u3057\u3066\u51e6\u65b9\u3055\u308c\u308b\u53ef\u80fd\u6027\u304c\u3042\u308b\u3068\u306e\u6700\u65b0\u60c5\u5831\u3092\u5831\u544a\u3057\u307e\u3057\u305f\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u8840\u6f3f\u5206\u753b\u304a\u3088\u3073\u63a1\u53d6\u6280\u8853\u3078\u306e\u6295\u8cc7\u306e\u5897\u52a0\u306b\u3088\u308a\u3001\u8840\u6f3f\u7531\u6765\u306eC1\u963b\u5bb3\u5264\u306e\u7d14\u5ea6\u304a\u3088\u3073\u53ce\u91cf\u304c\u5897\u52a0\u3057\u3066\u304a\u308a\u3001\u8840\u6f3f\u7531\u6765\u306e\u6cbb\u7642\u85ac\u306b\u5bfe\u3059\u308b\u9700\u8981\u3092\u727d\u5f15\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u306f\u3001\u5264\u5f62\u306b\u3088\u3063\u3066\u51cd\u7d50\u4e7e\u71e5\u54c1\u3068\u6ce8\u5c04\u5264\u306b\u4e8c\u5206\u3055\u308c\u307e\u3059\u30022024\u5e74\u306e\u58f2\u4e0a\u30b7\u30a7\u30a2\u306f\u51cd\u7d50\u4e7e\u71e5\u88fd\u5264\u304c61.2%\u3067\u6700\u5927\u3002<\/p>\n

\u51cd\u7d50\u4e7e\u71e5\u88fd\u5264\u306f\u51b7\u8535\u305b\u305a\u306b\u4fdd\u5b58\u3067\u304d\u308b\u305f\u3081\u3001\u533b\u7642\u5f93\u4e8b\u8005\u3084\u60a3\u8005\u306e\u9593\u3067\u4eba\u6c17\u304c\u3042\u308a\u307e\u3059\u3002\u3053\u308c\u306f\u3001\u9069\u5207\u306a\u30b3\u30fc\u30eb\u30c9\u30c1\u30a7\u30fc\u30f3\u306e\u30a4\u30f3\u30d5\u30e9\u304c\u6574\u5099\u3055\u308c\u3066\u3044\u306a\u3044\u5730\u65b9\u3067\u306f\u7279\u306b\u6709\u76ca\u3067\u3042\u308a\u3001\u3088\u308a\u9577\u3044\u4fdd\u5b58\u671f\u9593\u3068\u6d41\u901a\u80fd\u529b\u306e\u5411\u4e0a\u3092\u4fdd\u8a3c\u3057\u307e\u3059\u3002Cinryze\uff08\u6b66\u7530\u85ac\u54c1\u5de5\u696d\uff09\u3068Berinert\uff08CSL Behring\uff09\u306f\u3001\u5e83\u304f\u4f7f\u7528\u3055\u308c\u3066\u3044\u308b\u51cd\u7d50\u4e7e\u71e5C1-INH\u88fd\u54c1\u306e\u4e3b\u306a\u4f8b\u3067\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u51cd\u7d50\u4e7e\u71e5C1\u963b\u5bb3\u5264\u306e\u7528\u9014\u3092\u79fb\u690d\u62d2\u7d76\u53cd\u5fdc\u3001\u865a\u8840\u518d\u704c\u6d41\u969c\u5bb3\u3001\u6557\u8840\u75c7\u306a\u3069\u306e\u514d\u75ab\u95a2\u9023\u75be\u60a3\u3084\u708e\u75c7\u6027\u75be\u60a3\u306b\u62e1\u5927\u3059\u308b\u3053\u3068\u3092\u76ee\u6307\u3057\u305f\u7814\u7a76\u958b\u767a\u30a4\u30cb\u30b7\u30a2\u30c1\u30d6\u3082\u3042\u308a\u307e\u3059\u3002<\/p>\n

\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u85ac\u5e02\u5834\u306f\u3001\u6d41\u901a\u30c1\u30e3\u30cd\u30eb\u5225\u306b\u75c5\u9662\u85ac\u5c40\u3001\u5c0f\u58f2\u85ac\u5c40\u3001\u96fb\u5b50\u5546\u53d6\u5f15\u306b\u533a\u5206\u3055\u308c\u307e\u3059\u3002\u75c5\u9662\u85ac\u5c40\u90e8\u9580\u304c\u5e02\u5834\u3092\u652f\u914d\u3057\u30012024\u5e74\u306e\u58f2\u4e0a\u9ad8\u306f12\u5104\u7c73\u30c9\u30eb\u304c\u6700\u5927\u3002<\/p>\n

\u6025\u6027HAE\u767a\u4f5c\u306f\u3001\u6cbb\u7642\u305b\u305a\u306b\u653e\u7f6e\u3057\u3066\u304a\u304f\u3068\u81f4\u547d\u7684\u306b\u306a\u308b\u53ef\u80fd\u6027\u304c\u3042\u308a\u3001\u305d\u306e\u305f\u3081\u3001HAE\u767a\u4f5c\u306e\u5236\u5fa1\u306b\u304a\u3051\u308b\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306e\u91cd\u8981\u6027\u304c\u5f37\u8abf\u3055\u308c\u3066\u3044\u307e\u3059\u3002\u75c5\u9662\u85ac\u5c40\u306f\u3001\u7dca\u6025\u306eHAE\u767a\u4f5c\u75c7\u4f8b\u306b\u7dca\u6025\u306b\u5bfe\u5fdc\u3067\u304d\u308b\u305f\u3081\u3001\u91cd\u8981\u306a\u6d41\u901a\u624b\u6bb5\u3067\u3059\u3002
\n\u3055\u3089\u306b\u3001\u591a\u304f\u306eC1-INH\u6cbb\u7642\u85ac\u306f\u51cd\u7d50\u4e7e\u71e5\u54c1\u3067\u3042\u308a\u3001\u9759\u8108\u5185\u6295\u4e0e\u304c\u5fc5\u8981\u306a\u305f\u3081\u3001\u75c5\u9662\u304c\u6cbb\u7642\u306e\u4e2d\u5fc3\u3068\u306a\u3063\u3066\u3044\u307e\u3059\u3002\u305d\u306e\u305f\u3081\u3001\u591a\u304f\u306e\u88fd\u5264\u3001\u7279\u306bBerinert\u3084Ruconest\u306e\u3088\u3046\u306a\u70b9\u6ef4\u88fd\u5264\u306f\u3001\u75c5\u9662\u306e\u85ac\u5c40\u3067\u983b\u7e41\u306b\u5165\u624b\u53ef\u80fd\u3067\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u8840\u6f3f\u4e2d\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306f\u3001\u305d\u306e\u751f\u7269\u5b66\u7684\u6027\u8cea\u306e\u305f\u3081\u3001\u7279\u5b9a\u306e\u9001\u9054\u3001\u4fdd\u7ba1\u3001\u53d6\u308a\u6271\u3044\u624b\u9806\u304c\u5fc5\u8981\u3067\u3059\u3002\u75c5\u9662\u85ac\u5c40\u306f\u3001\u5fc5\u8981\u306a\u4fdd\u7ba1\u30ac\u30a4\u30c9\u30e9\u30a4\u30f3\u3092\u9075\u5b88\u3059\u308b\u305f\u3081\u306b\u5fc5\u8981\u306a\u30a4\u30f3\u30d5\u30e9\u3068\u8a2d\u5099\u3092\u6709\u3057\u3066\u304a\u308a\u3001\u88fd\u54c1\u306e\u5b8c\u5168\u6027\u3092\u78ba\u4fdd\u3057\u3001\u4e0d\u5fc5\u8981\u306a\u30ea\u30b9\u30af\u3092\u8efd\u6e1b\u3057\u307e\u3059\u3002<\/p>\n

\u30a2\u30e1\u30ea\u30ab\u306e\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u306e\u58f2\u4e0a\u306f\u30012024\u5e74\u306e7,294\u5104\u7c73\u30c9\u30eb\u304b\u3089\u5927\u5e45\u306b\u5897\u52a0\u3057\u30012034\u5e74\u306b\u306f18\u5104\u7c73\u30c9\u30eb\u306b\u9054\u3059\u308b\u898b\u8fbc\u307f\u3067\u3059\u3002<\/p>\n

\u30a2\u30e1\u30ea\u30ab\u3067\u306f\u3001HAE\u306e\u9ad8\u3044\u6709\u75c5\u7387\u3001\u30bf\u30a4\u30e0\u30ea\u30fc\u306a\u6cbb\u7642\u306b\u5bfe\u3059\u308b\u610f\u8b58\u306e\u9ad8\u307e\u308a\u3001\u907a\u4f1d\u5b50\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u306e\u5897\u52a0\u3001\u533b\u7642\u30a2\u30af\u30bb\u30b9\u306e\u62e1\u5927\u306a\u3069\u3001\u69d8\u3005\u306a\u8981\u56e0\u304b\u3089HAE\u6cbb\u7642\u306b\u5bfe\u3059\u308b\u9700\u8981\u304c\u9ad8\u307e\u3063\u3066\u304a\u308a\u3001\u3053\u306e\u5730\u57df\u306e\u5e02\u5834\u6210\u9577\u3092\u727d\u5f15\u3057\u3066\u3044\u307e\u3059\u3002\u4f8b\u3048\u3070\u3001Discover HAE\u306b\u3088\u308b\u3068\u3001\u30a2\u30e1\u30ea\u30ab\u3067\u306f\u7d046000\u4eba\u304cHAE\u306b\u7f79\u60a3\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u307e\u305f\u3001\u30a2\u30e1\u30ea\u30abFDA\u306e\u3088\u3046\u306a\u898f\u5236\u5f53\u5c40\u306f\u3001C1\u963b\u5bb3\u5264\u306e\u3088\u3046\u306a\u5e0c\u5c11\u306a\u6a19\u7684\u6cbb\u7642\u85ac\u306b\u5bfe\u3057\u3066\u3001\u30aa\u30fc\u30d5\u30a1\u30f3\u30c9\u30e9\u30c3\u30b0\u6307\u5b9a\u3084\u8fc5\u901f\u627f\u8a8d\u3092\u884c\u3063\u3066\u3044\u307e\u3059\u3002\u4f8b\u3048\u3070\u30012020\u5e749\u6708\u3001\u30a2\u30e1\u30ea\u30abFDA\u306f\u30016\u6b73\u4ee5\u4e0a\u306e\u60a3\u8005\u306eHAE\u767a\u4f5c\u3092\u4e88\u9632\u3059\u308bHAEGARDA\u306e\u627f\u8a8d\u3092\u767a\u8868\u3057\u307e\u3057\u305f\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u30a2\u30e1\u30ea\u30ab\u306b\u306f\u3001\u6b66\u7530\u85ac\u54c1\u5de5\u696d\u3001CSL\u30d9\u30fc\u30ea\u30f3\u30b0\u3001\u30d5\u30a1\u30fc\u30df\u30f3\u30b0\u30fb\u30b0\u30eb\u30fc\u30d7\u3001\u30ab\u30eb\u30d3\u30b9\u30bf\u30fb\u30d5\u30a1\u30fc\u30de\u30b7\u30e5\u30fc\u30c6\u30a3\u30ab\u30eb\u30ba\u306a\u3069\u306e\u5927\u624b\u4f01\u696d\u304c\u5b58\u5728\u3057\u3001\u7814\u7a76\u958b\u767a\u3084\u81e8\u5e8a\u8a66\u9a13\u3078\u306e\u6295\u8cc7\u3092\u63a8\u9032\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u30e8\u30fc\u30ed\u30c3\u30d1 \u82f1\u56fd\u306e\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u306f\u30012025\u5e74\u304b\u30892034\u5e74\u306b\u304b\u3051\u3066\u5927\u304d\u306a\u6210\u9577\u304c\u671f\u5f85\u3055\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u82f1\u56fd\u306e\u56fd\u6c11\u4fdd\u5065\u30b5\u30fc\u30d3\u30b9(NHS)\u306f\u56fd\u6c11\u7686\u4fdd\u967a\u5236\u5ea6\u3092\u63a1\u7528\u3057\u3066\u304a\u308a\u3001C1-INH\u3084\u30ab\u30ea\u30af\u30ec\u30a4\u30f3\u963b\u5bb3\u5264\u306e\u3088\u3046\u306a\u9ad8\u4fa1\u306a\u751f\u7269\u5b66\u7684\u88fd\u5264\u3092\u60a3\u8005\u304c\u5e83\u304f\u5229\u7528\u3067\u304d\u308b\u3088\u3046\u306b\u3057\u3066\u3044\u307e\u3059\u3002\u30a4\u30ae\u30ea\u30b9\u306b\u306f\u3001HAE UK\u306e\u3088\u3046\u306aHAE\u5c02\u9580\u6cbb\u7642\u30bb\u30f3\u30bf\u30fc\u304c\u3042\u308a\u3001\u30e8\u30fc\u30ed\u30c3\u30d1\u306b\u304a\u3051\u308bHAE\u7ba1\u7406\u306e\u4e3b\u8981\u306a\u76ee\u7684\u5730\u3068\u306a\u3063\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001NHS\u3084National Institute for Health and Care Excellence (NICE)\u304c\u63d0\u4f9b\u3059\u308b\u30ac\u30a4\u30c9\u30e9\u30a4\u30f3\u3084\u63a8\u5968\u306b\u3088\u308a\u3001\u82f1\u56fd\u3067\u306f\u533b\u7642\u74b0\u5883\u5168\u4f53\u3067\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u6cbb\u7642\u304c\u5e83\u304f\u63a1\u7528\u3055\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u82f1\u56fd\u3067\u306f\u96fb\u5b50\u5546\u53d6\u5f15\u306e\u666e\u53ca\u304c\u9032\u3093\u3067\u304a\u308a\u3001C1\u963b\u5bb3\u85ac\u306e\u81ea\u5df1\u6295\u4e0e\u304c\u53ef\u80fd\u306b\u306a\u3063\u3066\u3044\u308b\u3053\u3068\u3082\u3001\u82f1\u56fd\u306b\u304a\u3051\u308bHAE\u306e\u5728\u5b85C1\u963b\u5bb3\u85ac\u6cbb\u7642\u306e\u9700\u8981\u3092\u5f8c\u62bc\u3057\u3057\u3066\u3044\u307e\u3059\u3002\u82f1\u56fd\u306f\u3001\u4e3b\u8981\u306aC1-INH\u7642\u6cd5\u3092\u627f\u8a8d\u3057\u305f\u6700\u521d\u306e\u6b27\u5dde\u8af8\u56fd\u306e\u3072\u3068\u3064\u3067\u3059\u3002<\/p>\n

\u30a2\u30b8\u30a2\u592a\u5e73\u6d0b\u5730\u57df\uff1a \u65e5\u672c\u306e\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u306f\u30012025\u5e74\u304b\u30892034\u5e74\u306e\u9593\u306b\u6709\u5229\u306a\u6210\u9577\u3092\u9042\u3052\u308b\u3068\u4e88\u60f3\u3055\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u65e5\u672c\u306f\u9ad8\u5ea6\u306a\u533b\u7642\u30a4\u30f3\u30d5\u30e9\u3092\u6709\u3057\u3001\u9ad8\u5ea6\u306a\u8a3a\u65ad\u80fd\u529b\u3068\u5e83\u7bc4\u306a\u6d41\u901a\u7db2\u3092\u5099\u3048\u3066\u3044\u307e\u3059\u3002\u3055\u3089\u306b\u3001\u65e5\u672c\u3067\u306fHAE\u767a\u4f5c\u306e\u9577\u671f\u4e88\u9632\u306b\u7279\u5316\u3057\u305f\u81e8\u5e8a\u958b\u767a\u30d7\u30ed\u30b0\u30e9\u30e0\u304c\u9032\u884c\u4e2d\u3067\u3059\u3002\u3053\u308c\u3089\u306e\u8981\u56e0\u306b\u3088\u308a\u3001\u65e5\u672c\u3067\u306fHAE\u306e\u6cbb\u7642\u306b\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u306e\u63a1\u7528\u304c\u4fc3\u9032\u3055\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u65e5\u672c\u306b\u306f\u3001HAE\u6cbb\u7642\u3001\u907a\u4f1d\u5b50\u6cbb\u7642\u3001\u30e2\u30ce\u30af\u30ed\u30fc\u30ca\u30eb\u6297\u4f53\u306b\u95a2\u3059\u308b\u5148\u9032\u7684\u306a\u7814\u7a76\u65bd\u8a2d\u304c\u3042\u308a\u307e\u3059\u3002\u6771\u4eac\u5927\u5b66\u3084\u4eac\u90fd\u5927\u5b66\u306e\u3088\u3046\u306a\u65e5\u672c\u306e\u4e3b\u8981\u5927\u5b66\u306f\u3001\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bc\u963b\u5bb3\u5264\u3092\u8a66\u9a13\u3059\u308b\u56fd\u969b\u7684\u306a\u81e8\u5e8a\u7814\u7a76\u306b\u53c2\u52a0\u3057\u3066\u3044\u307e\u3059\u3002\u65e5\u672c\u306e\u88fd\u85ac\u30a8\u30b3\u30b7\u30b9\u30c6\u30e0\u306f\u30a4\u30ce\u30d9\u30fc\u30b7\u30e7\u30f3\u3092\u4fc3\u9032\u3057\u3001\u65e5\u672c\u306b\u304a\u3051\u308b\u907a\u4f1d\u5b50\u7d44\u63db\u3048\u578b\u304a\u3088\u3073\u7d4c\u53e3\u30d7\u30ed\u30c6\u30a2\u30fc\u30bc\u963b\u5bb3\u5264\u306e\u4f7f\u7528\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u307e\u305f\u3001\u30b7\u30f3\u30e9\u30a4\u30ba\u3001\u30d5\u30a3\u30e9\u30b8\u30fc\u30eb\u3001\u30ab\u30eb\u30d3\u30c8\u30fc\u30eb\u306e\u958b\u767a\u5143\u3067\u3042\u308b\u6b66\u7530\u85ac\u54c1\u5de5\u696d\u304c\u65e5\u672c\u306b\u9032\u51fa\u3057\u3066\u3044\u308b\u3053\u3068\u3082\u3001\u65e5\u672c\u306b\u304a\u3051\u308b\u5e02\u5834\u6210\u9577\u306e\u4e3b\u306a\u63a8\u9032\u8981\u56e0\u306e\u4e00\u3064\u3067\u3059\u3002<\/p>\n

\u4e2d\u6771\u30fb\u30a2\u30d5\u30ea\u30ab \u30b5\u30a6\u30b8\u30a2\u30e9\u30d3\u30a2\u306e\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u306f\u30012025\u5e74\u304b\u30892034\u5e74\u306b\u304b\u3051\u3066\u5927\u5e45\u304b\u3064\u6709\u671b\u306a\u6210\u9577\u304c\u898b\u8fbc\u307e\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

National Guard Health Affairs\u3001King Faisal Specialist Hospital & Research Centre\u3001King Fahad Medical City\u306a\u3069\u306e\u7d44\u7e54\u306b\u304a\u3051\u308b\u5c02\u7528\u7814\u7a76\u30bb\u30f3\u30bf\u30fc\u306e\u8a2d\u7acb\u3092\u901a\u3058\u305f\u533b\u7642\u30a4\u30f3\u30d5\u30e9\u3078\u306e\u591a\u984d\u306e\u6295\u8cc7\u304c\u3001\u69d8\u3005\u306a\u65b0\u898f\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u85ac\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u3068\u81e8\u5e8a\u7814\u7a76\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u3055\u3089\u306b\u3001\u56fd\u6c11\u3084\u533b\u7642\u5c02\u9580\u5bb6\u306e\u9593\u3067HAE\u306b\u95a2\u3059\u308b\u8a8d\u8b58\u304c\u9ad8\u307e\u3063\u3066\u3044\u308b\u3053\u3068\u304c\u3001\u8a3a\u65ad\u7387\u3092\u4fc3\u9032\u3057\u3001\u305d\u308c\u306b\u3088\u3063\u3066\u3053\u306e\u5730\u57df\u306b\u304a\u3051\u308b\u52b9\u679c\u7684\u306a\u6cbb\u7642\u30aa\u30d7\u30b7\u30e7\u30f3\u306e\u9700\u8981\u3092\u4fc3\u9032\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u30b7\u30a7\u30a2
\n\u5e02\u5834\u306f\u96c6\u4e2d\u3057\u3066\u304a\u308a\u3001\u627f\u8a8d\u88fd\u54c1\u3092\u6709\u3059\u308b\u88fd\u85ac\u4f01\u696d\u306f4\u793e\u3002CSL\u30d9\u30fc\u30ea\u30f3\u30b0\u3001\u30d0\u30a4\u30aa\u30af\u30ea\u30b9\u30c8\u30fb\u30d5\u30a1\u30fc\u30de\u30b7\u30e5\u30fc\u30c6\u30a3\u30ab\u30eb\u30ba\u3001\u30d5\u30a1\u30fc\u30df\u30f3\u30b0\u3001\u6b66\u7530\u85ac\u54c1\u5de5\u696d\u306e4\u793e\u304c\u5546\u696d\u5316\u88fd\u54c1\u3092\u6709\u3059\u308b\u552f\u4e00\u306e\u88fd\u85ac\u4f01\u696d\u3067\u3042\u308a\u3001\u5e02\u5834\u30b7\u30a7\u30a2\u306e100%\u3092\u5360\u3081\u3066\u3044\u307e\u3059\u3002\u3053\u308c\u3089\u306e\u30d7\u30ec\u30fc\u30e4\u30fc\u306f\u3001\u6cbb\u7642\u52b9\u7387\u3092\u9ad8\u3081\u308b\u305f\u3081\u306b\u5148\u9032\u7684\u306a\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u306b\u6295\u8cc7\u3057\u3066\u3044\u307e\u3059\u3002\u3055\u3089\u306b\u3001\u7814\u7a76\u6a5f\u95a2\u3084\u533b\u7642\u63d0\u4f9b\u8005\u3068\u306e\u6226\u7565\u7684\u30d1\u30fc\u30c8\u30ca\u30fc\u30b7\u30c3\u30d7\u306f\u3001\u6700\u65b0\u6280\u8853\u306e\u7d71\u5408\u3084\u6d41\u901a\u306e\u62e1\u5927\u306b\u4e0d\u53ef\u6b20\u3067\u3042\u308a\u3001\u3053\u308c\u306b\u3088\u3063\u3066\u5404\u793e\u306f\u6cbb\u7642\u30aa\u30d7\u30b7\u30e7\u30f3\u306b\u5bfe\u3059\u308b\u9700\u8981\u306e\u6025\u5897\u306b\u5bfe\u5fdc\u3067\u304d\u308b\u3088\u3046\u306b\u306a\u308a\u307e\u3057\u305f\u3002\u5e02\u5834\u306f\u3001\u898f\u5236\u5f53\u5c40\u306e\u652f\u63f4\u3068\u5408\u7406\u5316\u3055\u308c\u305f\u627f\u8a8d\u30d7\u30ed\u30bb\u30b9\u3092\u7d4c\u9a13\u3057\u3066\u304a\u308a\u3001\u3053\u308c\u304c\u3055\u3089\u306b\u6280\u8853\u9769\u65b0\u3078\u306e\u610f\u6b32\u3092\u9ad8\u3081\u3001\u5e02\u5834\u53c2\u5165\u3092\u5bb9\u6613\u306b\u3057\u3066\u3044\u307e\u3059\u3002\u3055\u3089\u306b\u3001\u65b0\u8208\u4f01\u696d\u306f\u75be\u75c5\u7ba1\u7406\u306e\u6539\u5584\u3092\u76ee\u7684\u3068\u3057\u305f\u65b0\u305f\u306a\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u306b\u6ce8\u529b\u3057\u3066\u3044\u307e\u3059\u3002\u3053\u306e\u3088\u3046\u306a\u6280\u8853\u9769\u65b0\u306f\u3001\u5e02\u5834\u306e\u62e1\u5927\u3092\u4fc3\u9032\u3057\u7d9a\u3051\u3066\u3044\u307e\u3059\u3002<\/p>\n

\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u53c2\u5165\u4f01\u696d
\n\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u696d\u754c\u3067\u4e8b\u696d\u3092\u5c55\u958b\u3059\u308b\u8457\u540d\u306a\u5e02\u5834\u53c2\u5165\u4f01\u696d\u306b\u306f\u3001\u4ee5\u4e0b\u306e\u3088\u3046\u306a\u3082\u306e\u304c\u3042\u308a\u307e\u3059\uff1a<\/p>\n

Astria
\nBioCryst Pharmaceuticals
\nCSL Behring
\nFresenius Kabi
\nIonis Pharmaceuticals
\nKalVista
\nPharming
\nPharvaris
\nTakeda Pharmaceutical Company<\/p>\n

CSL\u30d9\u30fc\u30ea\u30f3\u30b0\u306f\u3001\u8840\u6f3f\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u5264\u5e02\u5834\u306b\u304a\u3051\u308b\u4e3b\u8981\u306a\u30ea\u30fc\u30c0\u30fc\u3067\u3059\u3002\u540c\u793e\u306e\u4e3b\u529b\u88fd\u54c1\u3067\u3042\u308bBerinert\u306f\u3001HAE\u3092\u9069\u5fdc\u75c7\u3068\u3059\u308b\u4e00\u822c\u7684\u306aC1\u963b\u5bb3\u5264\u3067\u3059\u3002\u540c\u793e\u306e\u9ad8\u5ea6\u306a\u7814\u7a76\u958b\u767a\u80fd\u529b\u3068\u9ad8\u5ea6\u306a\u8ca9\u58f2\u7db2\u306f\u3001\u5e02\u5834\u3067\u306e\u30ea\u30fc\u30c0\u30fc\u30b7\u30c3\u30d7\u3092\u78ba\u56fa\u305f\u308b\u3082\u306e\u306b\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n

BioCryst Pharmaceuticals\u793e\u3082\u307e\u305f\u3001\u7d4c\u53e3\u8840\u6f3f\u30ab\u30ea\u30b9\u30de\u6cbb\u7642\u85acOrladeyo(berotralstat)\u3067\u5e02\u5834\u3092\u30ea\u30fc\u30c9\u3059\u308b\u4f01\u696d\u3067\u3059\u3002\u3053\u308c\u306f\u3001HAE\u306e\u6cbb\u7642\u306b\u9069\u5fdc\u306e\u3042\u308b\u7d4c\u53e3\u8840\u6f3f\u30ab\u30ea\u30af\u30ec\u30a4\u30f3\u963b\u5bb3\u5264\u3067\u3059\u3002\u6b66\u7530\u85ac\u54c1\u5de5\u696d\u306f\u3001HAE\u306e\u6cbb\u7642\u6210\u7e3e\u3092\u5411\u4e0a\u3055\u305b\u308b\u65b0\u898f\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u306b\u5411\u3051\u305f\u53d6\u308a\u7d44\u307f\u3092\u5f37\u5316\u3057\u3066\u304a\u308a\u3001\u540c\u5e02\u5834\u306b\u304a\u3051\u308b\u4e3b\u8981\u306a\u7af6\u5408\u4f01\u696d\u3068\u3057\u3066\u4f4d\u7f6e\u4ed8\u3051\u3089\u308c\u3066\u3044\u307e\u3059\u3002<\/p>\n

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\n2023\u5e745\u6708\u3001\u30d0\u30a4\u30aa\u30af\u30ea\u30b9\u30c8\u30fb\u30d5\u30a1\u30fc\u30de\u30b7\u30e5\u30fc\u30c6\u30a3\u30ab\u30eb\u30ba\u306f\u300112\u6b73\u4ee5\u4e0a\u306eHAE\u767a\u4f5c\u306b\u5bfe\u3059\u308b\u7d4c\u53e3\u6cbb\u7642\u85ac\u3067\u3042\u308b\u30aa\u30e9\u30c7\u30e8\uff08\u30d9\u30ed\u30c8\u30e9\u30eb\u30b9\u30bf\u30c3\u30c8\uff09\u304c\u30c1\u30ea\u306e\u516c\u8846\u885b\u751f\u7814\u7a76\u6240\uff08ISP\uff09\u304b\u3089\u8ca9\u58f2\u627f\u8a8d\u3092\u53d6\u5f97\u3057\u305f\u3053\u3068\u3092\u767a\u8868\u3057\u307e\u3057\u305f\u3002\u3053\u306e\u627f\u8a8d\u53d6\u5f97\u306b\u3088\u308a\u3001\u30d0\u30a4\u30aa\u30af\u30ea\u30b9\u30c8\u30d5\u30a1\u30fc\u30de\u306f\u3001\u672a\u958b\u62d3\u306e\u5e02\u5834\u3067\u3042\u308b\u4e2d\u5357\u7c73\u306e\u8840\u6f3f\u4e2d\u30d7\u30ed\u30c6\u30a2\u30fc\u30bcC1\u963b\u5bb3\u85ac\u5e02\u5834\u306b\u53c2\u5165\u3059\u308b\u3053\u3068\u306b\u306a\u308a\u307e\u3059\u3002<\/p>\n

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\n\u30a2\u30e9\u30d6\u9996\u9577\u56fd\u9023\u90a6<\/p>\n","protected":false},"author":4,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1],"tags":[],"aioseo_notices":[],"_links":{"self":[{"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/posts\/28983"}],"collection":[{"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/users\/4"}],"replies":[{"embeddable":true,"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/comments?post=28983"}],"version-history":[{"count":1,"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/posts\/28983\/revisions"}],"predecessor-version":[{"id":28984,"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/posts\/28983\/revisions\/28984"}],"wp:attachment":[{"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/media?parent=28983"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/categories?post=28983"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.marketresearch.jp\/reports\/wp-json\/wp\/v2\/tags?post=28983"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}